| Ultra-low dose chest CT for the diagnosis of pulmonary arteriovenous malformation in patients with hereditary hemorrhagic telangiectasia. | Delpon JE, Greffier J, Lacombe H, Barbe A, Bouin M, De Oliveira F, Mansuy A, Delagrange L, Fargeton AE, Beregi JP, Cottin V, Dupuis-Girod S, Si-Mohamed SA | 2024-04-10 | Diagnostic and interventional imaging |
| Phenotypes and outcome of diffuse pulmonary non-amyloid light chain deposition disease. | Lestelle F, Beigelman C, Rotzinger D, Si-Mohamed S, Nasser M, Wemeau L, Hirschi S, Prevot G, Roux A, Bunel V, Gomez E, Sohier L, Pradier HM, Gaubert MR, Gondouin A, Lazor R, Glerant JC, Bejui FT, Colombat M, Cottin V | 2024-04-10 | Respiratory research |
| High risk of lung cancer in surfactant-related gene variant carriers. | Brudon A, Legendre M, Mageau A, Bermudez J, Bonniaud P, Bouvry D, Cadranel J, Cazes A, Crestani B, Dégot T, Delestrain C, Diesler R, Epaud R, Philippot Q, Theou-Anton N, Kannengiesser C, Ba I, Debray MP, Fanen P, Manali E, Papiris S, Nathan N, Amselem S, Gondouin A, Guillaumot A, Andréjak C, Jouneau S, Beltramo G, Uzunhan Y, Galodé F, Westeel V, Mehdaoui A, Hirschi S, Leroy S, Marchand-Adam S, Nunes H, Picard C, Prevot G, Reynaud-Gaubert M, De Vuyst P, Wemeau L, Defossez G, Zalcman G, Cottin V, Borie R | 2024-04-04 | The European respiratory journal |
| Combined pulmonary fibrosis and emphysema syndrome: the age of majority. | Cottin V | 2024-04-01 | The European respiratory journal |
| PREFUL MRI for Monitoring Perfusion and Ventilation Changes after Elexacaftor-Tezacaftor-Ivacaftor Therapy for Cystic Fibrosis: A Feasibility Study. | Dohna M, Voskrebenzev A, Klimeš F, Kaireit TF, Glandorf J, Pallenberg ST, Ringshausen FC, Hansen G, Renz DM, Wacker F, Dittrich AM, Vogel-Claussen J | 2024-04-01 | Radiology. Cardiothoracic imaging |
| MERIT reloaded-what has changed in CTEPH management since 2017? | Torbicki A, Kurzyna M | 2024-04-01 | The Lancet. Respiratory medicine |
| Pulmonary vascular phenotype identified in patients with GDF2 (BMP9) or BMP10 variants: an international multicentre study. | Grynblat J, Bogaard HJ, Eyries M, Meyrignac O, Savale L, Jaïs X, Ghigna MR, Celant L, Meijboom L, Houweling AC, Levy M, Antigny F, Chaouat A, Cottin V, Guignabert C, Coulet F, Sitbon O, Bonnet D, Humbert M, Montani D | 2024-04-01 | The European respiratory journal |
| Quality of Life and the Cardiopulmonary Exercise Test in Pulmonary Arterial Hypertension Patients. | Martínez-Meñaca A, Mora-Cuesta VM, Iturbe-Fernández D, Sáinz-Ezquerra Belmonte B, Fernández-Cavia G, Gallardo-Ruiz MJ | 2024-04-01 | Archivos de bronconeumologia |
| Similarities and differences of interstitial lung disease associated with pathogenic variants in SFTPC and ABCA3 in adults. | Diesler R, Legendre M, Si-Mohamed S, Brillet PY, Wemeau L, Manali ED, Gagnadoux F, Hirschi S, Lorillon G, Reynaud-Gaubert M, Bironneau V, Blanchard E, Bourdin A, Dominique S, Justet A, Macey J, Marchand-Adam S, Morisse-Pradier H, Nunes H, Papiris SA, Traclet J, Traore I, Crestani B, Amselem S, Nathan N, Borie R, Cottin V | 2024-04-01 | Respirology (Carlton, Vic.) |
| Comment on the article titled "Impact of sex on outcome after pulmonary endarterectomy for chronic thromboembolic pulmonary hypertension" published by J. Chan et al. | Cruz-Utrilla A, López-Gude MJ, Velázquez M, Arribas-Ynsaurriaga F, Escribano-Subias P | 2024-04-01 | The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation |
| Clinical course of suspected familial and sporadic idiopathic pulmonary fibrosis: Data from the PROOF-Next registry. | Froidure A, Bondue B, Dahlqvist C, Guiot J, Gusbin N, Wirtz G, Brusselle G, Strens D, Slabbynck H, Wuyts WA | 2024-04-01 | Respirology (Carlton, Vic.) |
| Pulmonary Hypertension in Connective Tissue Diseases Other than Systemic Sclerosis. | Budhram B, Weatherald J, Humbert M | 2024-03-18 | Seminars in respiratory and critical care medicine |
| Chronic interstitial lung disease associated with systemic lupus erythematosus: A multicentric study of 89 cases. | Deneuville L, Mageau A, Debray MP, Sacre K, Costedoat-Chalumeau N, Hachulla E, Uzunhan Y, Le Tallec E, Cadranel J, Marchand Adam S, Montani D, Rémi-Jardin M, Reynaud-Gaubert M, Prevot G, Beltramo G, Crestani B, Cottin V, Borie R | 2024-03-17 | Respirology (Carlton, Vic.) |
| Pulmonary fibrosis is uncommon in primary Sjögren disease. | Si-Mohamed SA, Cottin V | 2024-03-15 | Diagnostic and interventional imaging |
| Health care resource utilization preceding death or lung transplantation in people with cystic fibrosis: HCRU before transplant or death in cystic fibrosis. | Guyot E, Reynaud Q, Belhassen M, Bérard M, Dehillotte C, Lemonnier L, Viprey M, Van Ganse E, Burgel PR, Durieu I | 2024-03-12 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Invasive Pulmonary Aspergillosis with Exclusive Pleural Involvement in a Lung Transplant Recipient. | García-Martín S, Mora-Cuesta VM, Naranjo-Gozalo S, Jiménez-Velasco JJ, Roiz-Mesones MP, Fernández-Lobo V | 2024-03-11 | Progress in transplantation (Aliso Viejo, Calif.) |
| Treatments for pulmonary arterial hypertension: navigating through a network of choices. | Pitre T, Weatherald J, Humbert M | 2024-03-05 | European heart journal |
| Corrigendum to "Expert management of congenital portosystemic shunts and their complications" [JHEP Reports 6 (2024)]. | McLin VA, Franchi-Abella S, Brütsch T, Bahadori A, Casotti V, de Ville de Goyet J, Dumery G, Gonzales E, Guérin F, Hascoet S, Heaton N, Kuhlmann B, Lador F, Lambert V, Marra P, Plessier DA, Quaglia A, Rougemont AL, Savale L, Sarma MS, Sitbon O, Superina RA, Uchida H, van Albada M, Johannes van der Doef HP, Vilgrain V, Wacker J, Zwaveling-Soonawala N, Debray D, Wildhaber BE | 2024-03-01 | JHEP reports : innovation in hepatology |
| Lumacaftor/Ivacaftor Population Pharmacokinetics in Pediatric Patients with Cystic Fibrosis: A First Step Toward Personalized Therapy. | Bouazza N, Urien S, Foissac F, Choupeaux L, Lui G, Froelicher Bournaud L, Rouillon S, Zheng Y, Bardin E, Stremler N, Bessaci K, Bihouee T, Coirier-Duet E, Marguet C, Deneuville E, Laurans M, Reix P, Gerardin M, Mittaine M, Epaud R, Thumerelle C, Weiss L, Berthaud R, Semeraro M, Treluyer JM, Benaboud S, Sermet-Gaudelus I | 2024-03-01 | Clinical pharmacokinetics |
| C-reactive protein as a candidate biomarker in fibrotic interstitial lung disease. | Cottin V, Valenzuela C | 2024-03-01 | Respirology (Carlton, Vic.) |
| Effect of Macitentan in Pulmonary Arterial Hypertension and the Relationship Between Echocardiography and cMRI Variables: REPAIR Echocardiography Sub-study Results. | Torbicki A, Channick R, Galiè N, Kiely DG, Moceri P, Peacock A, Swift AJ, Tawakol A, Vonk Noordegraaf A, Flores D, Martin N, Rosenkranz S | 2024-03-01 | Cardiology and therapy |
| Impact of Air Pollution and MUC5B Genotype on Survival in Idiopathic Pulmonary Fibrosis. | Sesé L, Borie R, Kannengiesser C, Cottin V, Israel-Biet D, Crestani B, Cadranel J, Chenivesse C, Boubaya M, Valeyre D, Annesi-Maesano I, Nunes H | 2024-03-01 | Annals of the American Thoracic Society |
| Risk Stratification in Pulmonary Veno-Occlusive Disease. | Cruz-Utrilla A, Pérez-Olivares C, Luna-López R, Jiménez López-Guarch C, Bedate P, Martínez Meñaca A, López Meseguer M, Escribano-Subias P | 2024-02-24 | Archivos de bronconeumologia |
| Zinpentraxin Alfa for Idiopathic Pulmonary Fibrosis: The Randomized Phase III STARSCAPE Trial. | Richeldi L, Schiffman C, Behr J, Inoue Y, Corte T, Cottin V, Jenkins RG, Nathan SD, Raghu G, Walsh SLF, Jayia PK, Kamath N, Martinez FJ | 2024-02-14 | American journal of respiratory and critical care medicine |
| Reversal of cylindrical bronchial dilatations in a subset of adults with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor. | Cazier P, Chassagnon G, Dhote T, Da Silva J, Kanaan R, Honore I, Carlier N, Revel MP, Canniff E, Martin C, Burgel PR | 2024-02-08 | The European respiratory journal |
| Role of Oxygen Starvation in Right Ventricular Decompensation and Failure in Pulmonary Arterial Hypertension. | Oknińska M, Zajda K, Zambrowska Z, Grzanka M, Paterek A, Mackiewicz U, Szczylik C, Kurzyna M, Piekiełko-Witkowska A, Torbicki A, Kieda C, Mączewski M | 2024-02-01 | JACC. Heart failure |
| A formula for predicting emphysema extent in combined idiopathic pulmonary fibrosis and emphysema. | Wells AU, Jacob J, Sverzellati N, Cross G, Barnett J, De Lauretis A, Antoniou K, Weycker D, Atwood M, Kirchgaessler KU, Cottin V | 2024-01-18 | Respiratory research |
| Publisher Correction: Pulmonary hypertension. | Mocumbi A, Humbert M, Saxena A, Jing ZC, Sliwa K, Thienemann F, Archer SL, Stewart S | 2024-01-17 | Nature reviews. Disease primers |
| Standards for the care of people with cystic fibrosis (CF); recognising and addressing CF health issues. | Burgel PR, Southern KW, Addy C, Battezzati A, Berry C, Bouchara JP, Brokaar E, Brown W, Azevedo P, Durieu I, Ekkelenkamp M, Finlayson F, Forton J, Gardecki J, Hodkova P, Hong G, Lowdon J, Madge S, Martin C, McKone E, Munck A, Ooi CY, Perrem L, Piper A, Prayle A, Ratjen F, Rosenfeld M, Sanders DB, Schwarz C, Taccetti G, Wainwright C, West NE, Wilschanski M, Bevan A, Castellani C, Drevinek P, Gartner S, Gramegna A, Lammertyn E, Landau EEC, Plant BJ, Smyth AR, van Koningsbruggen-Rietschel S, Middleton PG | 2024-01-16 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Pulmonary hypertension. | Mocumbi A, Humbert M, Saxena A, Jing ZC, Sliwa K, Thienemann F, Archer SL, Stewart S | 2024-01-04 | Nature reviews. Disease primers |
| Mepolizumab and benralizumab in patients with severe asthma and a history of eosinophilic granulomatosis with polyangiitis. | Desaintjean C, Ahmad K, Traclet J, Gerfaud-Valentin M, Durel CA, Glerant JC, Hot A, Lestelle F, Mainbourg S, Nasser M, Seve P, Turquier S, Devouassoux G, Cottin V | 2024-01-01 | Frontiers in medicine |
| Abnormal functional lymphoid tolerance and enhanced myeloid exocytosis are characteristics of resting and stimulated PBMCs in cystic fibrosis patients. | Gaudin C, Ghinnagow R, Lemaire F, Villeret B, Sermet-Gaudelus I, Sallenave JM | 2024-01-01 | Frontiers in immunology |
| Simplified risk stratification based on cardiopulmonary exercise test: A Spanish two-center experience. | Martínez-Meñaca A, Cruz-Utrilla A, Mora-Cuesta VM, Luna-López R, Segura-de la Cal T, Flox-Camacho Á, Alonso-Lecue P, Escribano-Subias P, Cifrián-Martínez JM | 2024-01-01 | Pulmonary circulation |
| Gathering real-world compassionate data to expand eligibility for elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis with N1303K or other rare CFTR variants: a viewpoint. | Burgel PR, Sermet-Gaudelus I, Girodon E, Kanaan R, Le Bihan J, Remus N, Ravoninjatovo B, Grenet D, Porzio M, Houdouin V, Le Clainche-Viala L, Durieu I, Nove-Josserand R, Languepin J, Coltey B, Guillaumot A, Audousset C, Chiron R, Weiss L, Fajac I, Da Silva J, Martin C | 2024-01-01 | The European respiratory journal |
| Expert management of congenital portosystemic shunts and their complications. | McLin VA, Franchi-Abella S, Brütsch T, Bahadori A, Casotti V, de Ville de Goyet J, Dumery G, Gonzales E, Guérin F, Hascoet S, Heaton N, Kuhlmann B, Lador F, Lambert V, Marra P, Plessier A, Quaglia A, Rougemont AL, Savale L, Sarma MS, Sitbon O, Superina RA, Uchida H, van Albada M, Johannes van der Doef HP, Vilgrain V, Wacker J, Zwaveling N, Debray D, Wildhaber BE | 2024-01-01 | JHEP reports : innovation in hepatology |
| A BEAT-PCD consensus statement: a core outcome set for pulmonary disease interventions in primary ciliary dyskinesia. | Kos R, Goutaki M, Kobbernagel HE, Rubbo B, Shoemark A, Aliberti S, Altenburg J, Anagnostopoulou P, Athanazio RA, Beydon N, Dell SD, Emiralioglu N, Ferkol TW, Loebinger MR, Lorent N, Maître B, Marthin J, Morgan LC, Nielsen KG, Ringshausen FC, Shteinberg M, Tiddens HAWM, Maitland-Van der Zee AH, Chalmers JD, Lucas JSA, Haarman EG | 2024-01-01 | ERJ open research |
| [Genetic diffuse cystic lung disease in adults]. | Diesler R, Ahmad K, Chalabreysse L, Glérant JC, Harzallah I, Touraine R, Si-Mohamed S, Cottin V | 2024-01-01 | Revue des maladies respiratoires |
| Infections in autoimmune pulmonary alveolar proteinosis: a large retrospective cohort. | Mabo A, Borie R, Wemeau-Stervinou L, Uzunhan Y, Gomez E, Prevot G, Reynaud-Gaubert M, Traclet J, Bergot E, Cadranel J, Marchand-Adam S, Bergeron A, Blanchard E, Bondue B, Bonniaud P, Bourdin A, Burgel PR, Hirschi S, Marquette CH, Quétant S, Nunes H, Chenivesse C, Crestani B, Guirriec Y, Monnier D, Ménard C, Tattevin P, Cottin V, Luque Paz D, Jouneau S | 2023-12-15 | Thorax |
| The Utility of a Resting Electrocardiogram (ECG-PH Index) in Evaluating the Efficacy of Pulmonary Endarterectomy in Chronic Thromboembolic Pulmonary Hypertension. | Piłka M, Darocha S, Florczyk M, Mańczak R, Banaszkiewicz M, Kędzierski P, Zieliński D, Wróbel K, Torbicki A, Kurzyna M | 2023-12-11 | Journal of clinical medicine |
| Rituximab to treat prolidase deficiency due to a novel pathogenic copy number variation in PEPD. | Atschekzei F, Fedchenko M, Elsayed A, Dubrowinskaja N, Graalmann T, Ringshausen FC, Witte T, Sogkas G | 2023-12-07 | RMD open |
| Long-term safety and efficacy of elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis and at least one F508del allele: 144-week interim results from a 192-week open-label extension study. | Daines CL, Tullis E, Costa S, Linnemann RW, Mall MA, McKone EF, Polineni D, Quon BS, Ringshausen FC, Rowe SM, Selvadurai H, Taylor-Cousar JL, Withers NJ, Ahluwalia N, Moskowitz SM, Prieto-Centurion V, Tan YV, Tian S, Weinstock T, Xuan F, Zhang Y, Ramsey B, Griese M | 2023-12-01 | The European respiratory journal |
| Monographic Issue on Pulmonary Hypertension. | Barberà JA, Humbert M | 2023-12-01 | Seminars in respiratory and critical care medicine |
| Extracorporeal Life Support in Pulmonary Hypertension: Practical Aspects. | Hoeper MM | 2023-12-01 | Seminars in respiratory and critical care medicine |
| Pulmonary Hypertension Associated with Left Heart Disease. | Baratto C, Caravita S, Vachiéry JL | 2023-12-01 | Seminars in respiratory and critical care medicine |
| Updated Hemodynamic Definition and Classification of Pulmonary Hypertension. | Lechartier B, Kularatne M, Jaïs X, Humbert M, Montani D | 2023-12-01 | Seminars in respiratory and critical care medicine |
| Monographic Issue on Pulmonary Hypertension: Medical and Interventional Treatment for Chronic Thromboembolic Pulmonary Hypertension. | Delcroix M, Belge C, Maleux G, Godinas L | 2023-12-01 | Seminars in respiratory and critical care medicine |
| The Right Ventricle in Pulmonary Hypertension. | Wessels JN, Celant LR, de Man FS, Vonk Noordegraaf A | 2023-12-01 | Seminars in respiratory and critical care medicine |
| Management of Pulmonary Hypertension Associated with Chronic Lung Disease. | Blanco I, Hernández-González F, García A, Torres-Castro R, Barberà JA | 2023-12-01 | Seminars in respiratory and critical care medicine |
| Management of Acutely Decompensated Pulmonary Hypertension. | Savale L, Kularatne M, Roche A, Pichon J, Baron A, Boucly A, Sitbon O, Humbert M | 2023-12-01 | Seminars in respiratory and critical care medicine |
| Ciliary Ultrastructure Assessed by Transmission Electron Microscopy in Adults with Bronchiectasis and Suspected Primary Ciliary Dyskinesia but Inconclusive Genotype. | Staar BO, Hegermann J, Auber B, Ewen R, von Hardenberg S, Olmer R, Pink I, Rademacher J, Wetzke M, Ringshausen FC | 2023-11-18 | Cells |
| Monitoring of ECFS quality standards for the clinical management of adults with cystic fibrosis. | Gramegna A, Aliberti S, Amorim A, Blasi F, Bourke S, Burgel PR, Diamantea F, Durieu I, Fila L, Moreno RMG, Messore B, Pokojová E, Taccetti G, Verhulst S, Dugac AV, Wege S, Duff A, Southern KW, Castellani C | 2023-11-08 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Leukocyte telomere length: the dawn of a new era of personalised medicine in fibrotic interstitial lung diseases? | Cottin V, Kolb M | 2023-11-01 | The European respiratory journal |
| Outcome of lung transplantation for adults with interstitial lung disease associated with genetic disorders of the surfactant system. | Bermudez J, Nathan N, Coiffard B, Roux A, Hirschi S, Degot T, Bunel V, Le Pavec J, Macey J, Le Borgne A, Legendre M, Cottin V, Thomas PA, Borie R, Reynaud-Gaubert M | 2023-11-01 | ERJ open research |
| Idiopathic pulmonary fibrosis with benign SFTPC variant and pathogenic MARS1 mutations: can't see the forest for the trees! | Castaldo A, Delestrain C, Diesler R, Merveilleux du Vignaux C, Onnee M, Touraine R, Chalabreysse L, Fanen P, Epaud R, Cottin V, De Becdelièvre A | 2023-11-01 | ERJ open research |
| Viewpoint: activin signalling inhibitors for the treatment of pulmonary arterial hypertension. | Humbert M | 2023-11-01 | The European respiratory journal |
| Defining the clinical validity of genes reported to cause pulmonary arterial hypertension. | Welch CL, Aldred MA, Balachandar S, Dooijes D, Eichstaedt CA, Gräf S, Houweling AC, Machado RD, Pandya D, Prapa M, Shaukat M, Southgate L, Tenorio-Castano J, Chung WK | 2023-11-01 | Genetics in medicine : official journal of the American College of Medical Genetics |
| Nonsense mutations accelerate lung disease and decrease survival of cystic fibrosis children. | Orenti A, Pranke I, Faucon C, Varilh J, Hatton A, Golec A, Dehillotte C, Durieu I, Reix P, Burgel PR, Grenet D, Tasset C, Gachelin E, Perisson C, Lepissier A, Dreano E, Tondelier D, Chevalier B, Weiss L, Kiefer S, Laurans M, Chiron R, Lemonnier L, Marguet C, Jung A, Edelman A, Kerem BS, Girodon E, Taulan-Cadars M, Hinzpeter A, Kerem E, Naehrlich L, Sermet-Gaudelus I | 2023-11-01 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Bronchial Stenosis After Lung Transplantation From cDCD Donors Using Simultaneous Abdominal Normothermic Regional Perfusion: A Single-center Experience. | Mora-Cuesta VM, Tello-Mena S, Izquierdo-Cuervo S, Iturbe-Fernández D, Sánchez-Moreno L, Ballesteros MA, Alonso-Lecue P, Ortíz-Portal F, Ferrer-Pargada D, Miñambres-García E, Cifrián-Martínez JM, Naranjo-Gozalo S | 2023-11-01 | Transplantation |
| Exploring intrinsic variability between cultured nasal and bronchial epithelia in cystic fibrosis. | Rodenburg LW, Metzemaekers M, van der Windt IS, Smits SMA, den Hertog-Oosterhoff LA, Kruisselbrink E, Brunsveld JE, Michel S, de Winter-de Groot KM, van der Ent CK, Stadhouders R, Beekman JM, Amatngalim GD | 2023-10-30 | Scientific reports |
| Seven Additional Patients with SOX17 Related Pulmonary Arterial Hypertension and Review of the Literature. | Gallego-Zazo N, Miranda-Alcaraz L, Cruz-Utrilla A, Del Cerro Marín MJ, Álvarez-Fuente M, Del Mar Rodríguez Vázquez Del Rey M, Guillén Rodríguez I, Becerra-Munoz VM, Moya-Bonora A, Ochoa Parra N, Parra A, Pascual P, Cazalla M, Silván C, Arias P, Valverde D, de Jesús-Pérez V, Lapunzina P, Escribano-Subías P, Tenorio-Castano J | 2023-10-20 | Genes |
| Theratyping cystic fibrosis patients to guide elexacaftor/tezacaftor/ivacaftor out-of-label prescription. | Dreano E, Burgel PR, Hatton A, Bouazza N, Chevalier B, Macey J, Leroy S, Durieu I, Weiss L, Grenet D, Stremler N, Ohlmann C, Reix P, Porzio M, Roux Claude P, Rémus N, Douvry B, Montcouquiol S, Cosson L, Mankikian J, Languepin J, Houdouin V, Le Clainche L, Guillaumot A, Pouradier D, Tissot A, Priou P, Mély L, Chedevergne F, Lebourgeois M, Lebihan J, Martin C, Zavala F, Da Silva J, Lemonnier L, Kelly-Aubert M, Golec A, Foucaud P, Marguet C, Edelman A, Hinzpeter A, de Carli P, Girodon E, Sermet-Gaudelus I, Pranke I | 2023-10-01 | The European respiratory journal |
| Prognostic Stratification and Treatment for Pulmonary Arterial Hypertension. Gaps and Promising Remedies. | Del Pozo R, Cruz-Utrilla A, Escribano-Subias P | 2023-10-01 | Archivos de bronconeumologia |
| Protocol for generating airway organoids from 2D air liquid interface-differentiated nasal epithelia for use in a functional CFTR assay. | Rodenburg LW, van der Windt IS, Dreyer HHM, Smits SMA, den Hertog-Oosterhoff LA, Aarts EM, Beekman JM, Amatngalim GD | 2023-09-15 | STAR protocols |
| The European reference network on rare lung diseases (ERN-LUNG) ambition to offer better lung health for all. | Humbert M, Wagner T | 2023-09-10 | Presse medicale (Paris, France : 1983) |
| Design of a phase III, double-blind, randomised, placebo-controlled trial of BI 1015550 in patients with progressive pulmonary fibrosis (FIBRONEER-ILD). | Maher TM, Assassi S, Azuma A, Cottin V, Hoffmann-Vold AM, Kreuter M, Oldham JM, Richeldi L, Valenzuela C, Wijsenbeek MS, Coeck C, Schlecker C, Voss F, Wachtlin D, Martinez FJ | 2023-09-01 | BMJ open respiratory research |
| Treatment of pulmonary arterial hypertension: recent progress and a look to the future. | Humbert M, Sitbon O, Guignabert C, Savale L, Boucly A, Gallant-Dewavrin M, McLaughlin V, Hoeper MM, Weatherald J | 2023-09-01 | The Lancet. Respiratory medicine |
| Interstitial lung disease-associated pulmonary hypertension - what the future holds. | Cottin V, Diesler R, Turquier S, Valenzuela C | 2023-09-01 | Current opinion in pulmonary medicine |
| Pulmonary alveolar proteinosis - current and future therapeutical strategies. | Jehn LB, Bonella F | 2023-09-01 | Current opinion in pulmonary medicine |
| Autoantibodies against the NineTeen complex and U5 RNP in systemic sclerosis. | Vulsteke JB, Smith V, Bonroy C, Lenaerts JL, Derua R, Wuyts WA, Blockmans D, De Haes P, Piette Y, De Langhe E, Bossuyt X | 2023-09-01 | Journal of autoimmunity |
| Comprehensive Clinical Diagnostic Pipelines Reveal New Variants in Alpha-1 Antitrypsin Deficiency. | Ottaviani S, Bartoli G, Carroll TP, Gangemi F, Balderacchi AM, Barzon V, Corino A, Piloni D, McElvaney NG, Corsico AG, Irving JA, Fra A, Ferrarotti I | 2023-09-01 | American journal of respiratory cell and molecular biology |
| Emerging Role of Balloon Pulmonary Angioplasty in Chronic Thromboembolic Pulmonary Disease-Insights from the 2022 ESC Guidelines. | Banaszkiewicz M, Kurzyna P, Kubikowska N, Mucha M, Rudnik A, Gąsecka A, Pietrasik A, Grabowski M, Jaguszewski MJ, Kasprzyk P, Kędzierski P, Ciećwierz D, Żuk G, Szwed P, Piłka M, Florczyk M, Kurzyna M, Darocha S | 2023-08-16 | Journal of clinical medicine |
| Design of a phase III, double-blind, randomised, placebo-controlled trial of BI 1015550 in patients with idiopathic pulmonary fibrosis (FIBRONEER-IPF). | Richeldi L, Azuma A, Cottin V, Kreuter M, Maher TM, Martinez FJ, Oldham JM, Valenzuela C, Gordat M, Liu Y, Stowasser S, Zoz DF, Wijsenbeek MS | 2023-08-01 | BMJ open respiratory research |
| Alpha1-antitrypsin deficiency: An updated review. | Mornex JF, Traclet J, Guillaud O, Dechomet M, Lombard C, Ruiz M, Revel D, Reix P, Cottin V | 2023-07-29 | Presse medicale (Paris, France : 1983) |
| Cystic fibrosis. | Fajac I, Burgel PR | 2023-07-27 | Presse medicale (Paris, France : 1983) |
| Optimal treatment of the underlying aetiology is the most effective antimicrobial stewardship for chronic respiratory disease: a lesson learned from cystic fibrosis. | Rademacher J, Martin L, Theloe A, Stahl M, Mall MA, Joean O, Fuge J, Hansen G, Welte T, Schütz K, Ringshausen FC, Dittrich AM | 2023-07-01 | ERJ open research |
| Diagnosis and management of pulmonary veno-occlusive disease. | Solinas S, Boucly A, Beurnier A, Kularatne M, Grynblat J, Eyries M, Dorfmüller P, Sitbon O, Humbert M, Montani D | 2023-07-01 | Expert review of respiratory medicine |
| Treatable traits: a comprehensive precision medicine approach in interstitial lung disease. | Khor YH, Cottin V, Holland AE, Inoue Y, McDonald VM, Oldham J, Renzoni EA, Russell AM, Strek ME, Ryerson CJ | 2023-07-01 | The European respiratory journal |
| Lung Function Decline in Cystic Fibrosis: Impact of Data Availability and Modeling Strategies on Clinical Interpretations. | Szczesniak R, Andrinopoulou ER, Su W, Afonso PM, Burgel PR, Cromwell E, Gecili E, Ghulam E, Goss CH, Mayer-Hamblett N, Keogh RH, Liou TG, Marshall B, Morgan WJ, Ostrenga JS, Pasta DJ, Stanojevic S, Wainwright C, Zhou GC, Fernandez G, Fink AK, Schechter MS | 2023-07-01 | Annals of the American Thoracic Society |
| CT imaging shows specific pancreatic abnormalities in persons with cystic fibrosis related diabetes. | Alexandre-Heymann L, Puerto M, Martin C, Burnet E, Mosnier-Pudar H, Burgel PR, Larger E | 2023-06-27 | Scientific reports |
| Inhaled treprostinil for interstitial lung disease-associated pulmonary hypertension: a silver lining on a very dark cloud. | Cottin V, Valenzuela C, Humbert M | 2023-06-01 | The European respiratory journal |
| Transforming clinical research and science in bronchiectasis: EMBARC3, a European Respiratory Society Clinical Research Collaboration. | Chalmers JD, Aliberti S, Altenburg J, Blasi F, Clarke C, Chotirmall SH, Crichton ML, Dhar R, Goeminne P, Haworth C, Loebinger MR, Lorent N, Polverino E, Ringshausen FC, Shoemark A, Shteinberg M, Sibila O, Spinou A, Welte T | 2023-06-01 | The European respiratory journal |
| Evidence-Based Guideline for the diagnosis and management of eosinophilic granulomatosis with polyangiitis. | Emmi G, Bettiol A, Gelain E, Bajema IM, Berti A, Burns S, Cid MC, Cohen Tervaert JW, Cottin V, Durante E, Holle JU, Mahr AD, Del Pero MM, Marvisi C, Mills J, Moiseev S, Moosig F, Mukhtyar C, Neumann T, Olivotto I, Salvarani C, Seeliger B, Sinico RA, Taillé C, Terrier B, Venhoff N, Bertsias G, Guillevin L, Jayne DRW, Vaglio A | 2023-06-01 | Nature reviews. Rheumatology |
| French recommendations for the diagnosis and management of lymphangioleiomyomatosis. | Cottin V, Blanchard E, Kerjouan M, Lazor R, Reynaud-Gaubert M, Taille C, Uzunhan Y, Wemeau L, Andrejak C, Baud D, Bonniaud P, Brillet PY, Calender A, Chalabreysse L, Court-Fortune I, Desbaillets NP, Ferretti G, Guillemot A, Hardelin L, Kambouchner M, Leclerc V, Lederlin M, Malinge MC, Mancel A, Marchand-Adam S, Maury JM, Naccache JM, Nasser M, Nunes H, Pagnoux G, Prévot G, Rousset-Jablonski C, Rouviere O, Si-Mohamed S, Touraine R, Traclet J, Turquier S, Vagnarelli S, Ahmad K | 2023-06-01 | Respiratory medicine and research |
| Validating organoid-derived human intestinal monolayers for personalized therapy in cystic fibrosis. | Birimberg-Schwartz L, Ip W, Bartlett C, Avolio J, Vonk AM, Gunawardena T, Du K, Esmaeili M, Beekman JM, Rommens J, Strug L, Bear CE, Moraes TJ, Gonska T | 2023-06-01 | Life science alliance |
| French practical guidelines for the diagnosis and management of idiopathic pulmonary fibrosis - 2021 update. Full-length version. | Cottin V, Bonniaud P, Cadranel J, Crestani B, Jouneau S, Marchand-Adam S, Nunes H, Wémeau-Stervinou L, Bergot E, Blanchard E, Borie R, Bourdin A, Chenivesse C, Clément A, Gomez E, Gondouin A, Hirschi S, Lebargy F, Marquette CH, Montani D, Prévot G, Quetant S, Reynaud-Gaubert M, Salaun M, Sanchez O, Trumbic B, Berkani K, Brillet PY, Campana M, Chalabreysse L, Chatté G, Debieuvre D, Ferretti G, Fourrier JM, Just N, Kambouchner M, Legrand B, Le Guillou F, Lhuillier JP, Mehdaoui A, Naccache JM, Paganon C, Rémy-Jardin M, Si-Mohamed S, Terrioux P | 2023-06-01 | Respiratory medicine and research |
| Usefulness of genetics for clinical reclassification and refinement of prognostic stratification in pulmonary arterial hypertension. | Cruz-Utrilla A, Gallego-Zazo N, Pérez-Olivares C, Hernández-González I, Bedate P, Martínez Meñaca A, López Meseguer M, Lapunzina P, Pérez Núñez M, Ochoa Parra N, Valverde D, Tenorio-Castaño JA, Escribano-Subias P | 2023-06-01 | Revista espanola de cardiologia (English ed.) |
| Primary Ciliary Dyskinesia Patient-Specific hiPSC-Derived Airway Epithelium in Air-Liquid Interface Culture Recapitulates Disease Specific Phenotypes In Vitro. | von Schledorn L, Puertollano Martín D, Cleve N, Zöllner J, Roth D, Staar BO, Hegermann J, Ringshausen FC, Nawroth J, Martin U, Olmer R | 2023-05-24 | Cells |
| Pseudomonas aeruginosa population genomics among adults with bronchiectasis across Germany. | Rosenboom I, Oguz S, Lüdemann IM, Ringshausen FC, Rademacher J, Sedlacek L, Tümmler B, Cramer N | 2023-05-01 | ERJ open research |
| The RISE study protocol: resilience impacted by positive stressful events for people with cystic fibrosis. | van der Heijden E, van den Bor RM, van der Ent CK, Nijhof SL, van der Laan SEI | 2023-05-01 | ERJ open research |
| The U UGA C sequence provides a favorable context to ELX-02 induced CFTR readthrough. | Pranke IM, Varilh J, Hatton A, Faucon C, Girodon E, Dreano E, Chevalier B, Karri S, Reix P, Durieu I, Bidou L, Namy O, Taulan M, Hinzpeter A, Sermet-Gaudelus I | 2023-05-01 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Long COVID syndrome after SARS-CoV-2 survival in patients with pulmonary arterial hypertension and chronic thromboembolic pulmonary hypertension. | Wieteska-Miłek M, Kuśmierczyk-Droszcz B, Betkier-Lipińska K, Szmit S, Florczyk M, Zieliński P, Hoffman P, Krzesińki P, Kurzyna M | 2023-04-01 | Pulmonary circulation |
| Epidemiological trends in nontuberculous mycobacterial infection among people with cystic fibrosis in Germany. | Steindor M, Hafkemeyer S, Ruckes C, Stehling F, Naehrlich L, Ringshausen FC | 2023-04-01 | International journal of infectious diseases : IJID : official publication of the International Society for Infectious Diseases |
| CFTR Modulators: Current Status and Evolving Knowledge. | Regard L, Martin C, Da Silva J, Burgel PR | 2023-04-01 | Seminars in respiratory and critical care medicine |
| The world of rare interstitial lung diseases. | Buschulte K, Cottin V, Wijsenbeek M, Kreuter M, Diesler R | 2023-03-31 | European respiratory review : an official journal of the European Respiratory Society |
| Ordinal outcomes add value to clinical trials - Authors' reply. | Weatherald J, Humbert M | 2023-03-25 | Lancet (London, England) |
| European Respiratory Society statement on familial pulmonary fibrosis. | Borie R, Kannengiesser C, Antoniou K, Bonella F, Crestani B, Fabre A, Froidure A, Galvin L, Griese M, Grutters JC, Molina-Molina M, Poletti V, Prasse A, Renzoni E, van der Smagt J, van Moorsel CHM | 2023-03-01 | The European respiratory journal |
| Progressive pulmonary fibrosis: an expert group consensus statement. | Rajan SK, Cottin V, Dhar R, Danoff S, Flaherty KR, Brown KK, Mohan A, Renzoni E, Mohan M, Udwadia Z, Shenoy P, Currow D, Devraj A, Jankharia B, Kulshrestha R, Jones S, Ravaglia C, Quadrelli S, Iyer R, Dhooria S, Kolb M, Wells AU | 2023-03-01 | The European respiratory journal |
| GLPG1205 for idiopathic pulmonary fibrosis: a phase 2 randomised placebo-controlled trial. | Strambu IR, Seemayer CA, Fagard LMA, Ford PA, Van der Aa TAK, de Haas-Amatsaleh AA, Modgill V, Santermans E, Sondag EN, Helmer EG, Maher TM, Costabel U, Cottin V | 2023-03-01 | The European respiratory journal |
| PDE5 to keep them alive: The use of phosphodiesterase type-5 inhibitors in severe pulmonary hypertension associated with interstitial lung disease. | Weatherald J, Humbert M | 2023-03-01 | Respirology (Carlton, Vic.) |
| Lung Dual-Energy CT Perfusion Blood Volume as a Marker of Severity in Chronic Thromboembolic Pulmonary Hypertension. | Si-Mohamed SA, Zumbihl L, Turquier S, Boccalini S, Mornex JF, Douek P, Cottin V, Boussel L | 2023-02-17 | Diagnostics (Basel, Switzerland) |
| The French Compassionate Program of elexacaftor-tezacaftor-ivacaftor in people with cystic fibrosis with advanced lung disease and no F508del CFTR variant. | Burgel PR, Sermet-Gaudelus I, Durieu I, Kanaan R, Macey J, Grenet D, Porzio M, Coolen-Allou N, Chiron R, Marguet C, Douvry B, Dufeu N, Danner-Boucher I, Foucaud P, Lemonnier L, Girodon E, Da Silva J, Martin C | 2023-02-16 | The European respiratory journal |
| Proteomic profiling of sweat in patients with cystic fibrosis provides new insights into epidermal homoeostasis. | Cornet M, Nguyen-Khoa T, Kelly-Aubert M, Jung V, Chedevergne F, Le Bourgeois M, Aoust L, Roger K, Guerrera CI, Sermet-Gaudelus I | 2023-02-01 | Skin health and disease |
| Identification of new telomere- and telomerase-associated autoantigens in systemic sclerosis. | Vulsteke JB, Smith V, Bonroy C, Derua R, Blockmans D, De Haes P, Vanderschueren S, Lenaerts JL, Claeys KG, Wuyts WA, Verschueren P, Vanhandsaeme G, Piette Y, De Langhe E, Bossuyt X | 2023-02-01 | Journal of autoimmunity |
| Towards Translation of PqsR Inverse Agonists: From In Vitro Efficacy Optimization to In Vivo Proof-of-Principle. | Hamed MM, Abdelsamie AS, Rox K, Schütz C, Kany AM, Röhrig T, Schmelz S, Blankenfeldt W, Arce-Rodriguez A, Borrero-de Acuña JM, Jahn D, Rademacher J, Ringshausen FC, Cramer N, Tümmler B, Hirsch AKH, Hartmann RW, Empting M | 2023-02-01 | Advanced science (Weinheim, Baden-Wurttemberg, Germany) |
| Qualitative and quantitative evaluation of computed tomography changes in adults with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor: a retrospective observational study. | Dettmer S, Weinheimer O, Sauer-Heilborn A, Lammers O, Wielpütz MO, Fuge J, Welte T, Wacker F, Ringshausen FC | 2023-01-01 | Frontiers in pharmacology |
| A practical approach to the 2022 ESC cardio-oncology guidelines: Comments by a team of experts - cardiologists and oncologists. | Leszek P, Klotzka A, Bartuś S, Burchardt P, Czarnecka AM, Długosz-Danecka M, Gierlotka M, Koseła-Paterczyk H, Krawczyk-Ożóg A, Kubiatowski T, Kurzyna M, Maciejczyk A, Mitkowski P, Prejbisz A, Rutkowski P, Sierko E, Sterliński M, Szmit S, Szwiec M, Tajstra M, Tycińska A, Witkowski A, Wojakowski W, Cybulska-Stopa B | 2023-01-01 | Kardiologia polska |
| Case report: Transected Hickman catheter and its thrombotic occlusion in a patient with idiopathic pulmonary arterial hypertension-can a catheter replacement be avoided? | Sławiński G, Zieleniewicz P, Faran A, Dąbrowska-Kugacka A, Kurzyna M, Kempa M, Daniłowicz-Szymanowicz L, Lewicka E | 2023-01-01 | Frontiers in cardiovascular medicine |
| Spirometric and anthropometric improvements in response to elexacaftor/tezacaftor/ivacaftor depending on age and lung disease severity. | Schütz K, Pallenberg ST, Kontsendorn J, DeLuca D, Sukdolak C, Minso R, Büttner T, Wetzke M, Dopfer C, Sauer-Heilborn A, Ringshausen FC, Junge S, Tümmler B, Hansen G, Dittrich AM | 2023-01-01 | Frontiers in pharmacology |
| ECMO in pulmonary arterial hypertension and chronic thromboembolic pulmonary hypertension as a bridge to therapy. | Cruz-Utrilla A, García-Martín EP, Domínguez Pérez L, Ruiz Curiel A, Quezada A, Durante López A, Vicent L, Martín Asenjo R, Hinojosa W, Eixerés A, Forcén Acebal L, Galindo M, Arribas Ynsaurriaga F, Escribano-Subias P, Bueno H | 2023-01-01 | Kardiologia polska |
| COVID-19 in patients with pulmonary alveolar proteinosis: a European multicentre study. | Papiris SA, Campo I, Mariani F, Kallieri M, Kolilekas L, Papaioannou AI, Gonca Chousein E, Cetinkaya E, Bonella F, Borie R, Kokosi M, Pickworth T, Molina-Molina M, Gasa M, Radzikowska E, Fijolek J, Jouneau S, Gomez E, McCarthy C, Bendstrup E, Piotrowski WJ, Pabary R, Hadchouel A, Coolen-Allou N, Alfaro T, Robalo Cordeiro C, Antonogiannaki EM, Tomos IP, Papakosta D, Kontakiotis T, Panagiotou P, Douros K, Schams A, Lettieri S, Papaevangelou V, Kanaka-Gantenbein C, Karakatsani A, Loukides S, Costabel U, Crestani B, Morgan C, Tazawa R, Bush A, Griese M, Manali ED | 2023-01-01 | ERJ open research |
| Lung transplantation for end-stage cystic fibrosis before and after the availability of elexacaftor-tezacaftor-ivacaftor, Germany, 2012-2021. | Ringshausen FC, Sauer-Heilborn A, Büttner T, Dittrich AM, Schwerk N, Ius F, Nährlich L, Welte T, Greer M | 2023-01-01 | The European respiratory journal |
| Normalisation of circulating neutrophil counts after 12 months of elexacaftor-tezacaftor-ivacaftor in patients with advanced cystic fibrosis. | Dhote T, Martin C, Regard L, Pesenti L, Kanaan R, Carlier N, Honoré I, Da Silva J, Witko-Sarsat V, Burgel PR | 2023-01-01 | The European respiratory journal |
| The Changing Epidemiology of Cystic Fibrosis: The Implications for Adult Care. | Burgel PR, Burnet E, Regard L, Martin C | 2023-01-01 | Chest |
| Crosstalk between cilia and autophagy: implication for human diseases. | Morleo M, Vieira HLA, Pennekamp P, Palma A, Bento-Lopes L, Omran H, Lopes SS, Barral DC, Franco B | 2023-01-01 | Autophagy |
| Redefining Hypo- and Hyper-Responding Phenotypes of CFTR Mutants for Understanding and Therapy. | Hillenaar T, Beekman J, van der Sluijs P, Braakman I | 2022-12-02 | International journal of molecular sciences |
| European Respiratory Society guidelines on transbronchial lung cryobiopsy in the diagnosis of interstitial lung diseases. | Korevaar DA, Colella S, Fally M, Camuset J, Colby TV, Hagmeyer L, Hetzel J, Maldonado F, Morais A, Ravaglia C, Spijker R, Tomassetti S, Troy LK, Verschakelen JA, Wells AU, Tonia T, Annema JT, Poletti V | 2022-11-01 | The European respiratory journal |
| Drug Repurposing for Cystic Fibrosis: Identification of Drugs That Induce CFTR-Independent Fluid Secretion in Nasal Organoids. | Rodenburg LW, Delpiano L, Railean V, Centeio R, Pinto MC, Smits SMA, van der Windt IS, van Hugten CFJ, van Beuningen SFB, Rodenburg RNP, van der Ent CK, Amaral MD, Kunzelmann K, Gray MA, Beekman JM, Amatngalim GD | 2022-10-21 | International journal of molecular sciences |
| Phenotypes of idiopathic pulmonary arterial hypertension. | Cruz-Utrilla A, Pérez-Olivares C, Martínez-Meñaca A, López-Meseguer M, Escribano-Subias P | 2022-10-01 | The Lancet. Respiratory medicine |
| Drug-induced interstitial lung disease. | Spagnolo P, Bonniaud P, Rossi G, Sverzellati N, Cottin V | 2022-10-01 | The European respiratory journal |
| Pharmacological chaperone-rescued cystic fibrosis CFTR-F508del mutant overcomes PRAF2-gated access to endoplasmic reticulum exit sites. | Saha K, Chevalier B, Doly S, Baatallah N, Guilbert T, Pranke I, Scott MGH, Enslen H, Guerrera C, Chuon C, Edelman A, Sermet-Gaudelus I, Hinzpeter A, Marullo S | 2022-09-27 | Cellular and molecular life sciences : CMLS |
| Clinical Implications of the Genetic Background in Pediatric Pulmonary Arterial Hypertension: Data from the Spanish REHIPED Registry. | Cruz-Utrilla A, Gallego-Zazo N, Tenorio-Castaño JA, Guillén I, Torrent-Vernetta A, Moya-Bonora A, Labrandero C, Rodríguez-Monte MEG, Rodríguez-Ogando A, Rey MDMRVD, Espín J, Plata-Izquierdo B, Álvarez-Fuente M, Moreno-Galdó A, Escribano-Subias P, Marín MJDC | 2022-09-09 | International journal of molecular sciences |
| [Test Your Knowledge]. | Angelini E, Dettmer S, Goecke T, Länger F, Ringshausen FC | 2022-09-01 | Pneumologie (Stuttgart, Germany) |
| Clinical impact of TERT somatic mutation in telomerase-related gene mutation carriers after lung transplantation. | Ba I, Kannengiesser C, Mal H, Reynaud-Gaubert M, Cottin V, Hirschi S, Picard C, Borie R | 2022-09-01 | The Journal of heart and lung transplantation : the official publication of the International Society for Heart Transplantation |
| [French practical guidelines for the diagnosis and management of IPF - 2021 update, full version]. | Cottin V, Bonniaud P, Cadranel J, Crestani B, Jouneau S, Marchand-Adam S, Nunes H, Wémeau-Stervinou L, Bergot E, Blanchard E, Borie R, Bourdin A, Chenivesse C, Clément A, Gomez E, Gondouin A, Hirschi S, Lebargy F, Marquette CH, Montani D, Prévot G, Quetant S, Reynaud-Gaubert M, Salaun M, Sanchez O, Trumbic B, Berkani K, Brillet PY, Campana M, Chalabreysse L, Chatté G, Debieuvre D, Ferretti G, Fourrier JM, Just N, Kambouchner M, Legrand B, Le Guillou F, Lhuillier JP, Mehdaoui A, Naccache JM, Paganon C, Rémy-Jardin M, Si-Mohamed S, Terrioux P | 2022-09-01 | Revue des maladies respiratoires |
| Differential CFTR-Interactome Proximity Labeling Procedures Identify Enrichment in Multiple SLC Transporters. | Chevalier B, Baatallah N, Najm M, Castanier S, Jung V, Pranke I, Golec A, Stoven V, Marullo S, Antigny F, Guerrera IC, Sermet-Gaudelus I, Edelman A, Hinzpeter A | 2022-08-11 | International journal of molecular sciences |
| Measuring cystic fibrosis drug responses in organoids derived from 2D differentiated nasal epithelia. | Amatngalim GD, Rodenburg LW, Aalbers BL, Raeven HH, Aarts EM, Sarhane D, Spelier S, Lefferts JW, Silva IA, Nijenhuis W, Vrendenbarg S, Kruisselbrink E, Brunsveld JE, van Drunen CM, Michel S, de Winter-de Groot KM, Heijerman HG, Kapitein LC, Amaral MD, van der Ent CK, Beekman JM | 2022-08-03 | Life science alliance |
| Integrating Clinical Probability into the Diagnostic Approach to Idiopathic Pulmonary Fibrosis: An International Working Group Perspective. | Cottin V, Tomassetti S, Valenzuela C, Walsh SLF, Antoniou KM, Bonella F, Brown KK, Collard HR, Corte TJ, Flaherty KR, Johannson KA, Kolb M, Kreuter M, Inoue Y, Jenkins RG, Lee JS, Lynch DA, Maher TM, Martinez FJ, Molina-Molina M, Myers JL, Nathan SD, Poletti V, Quadrelli S, Raghu G, Rajan SK, Ravaglia C, Remy-Jardin M, Renzoni E, Richeldi LK, Spagnolo P, Troy L, Wijsenbeek M, Wilson KC, Wuyts W, Wells AU, Ryerson CJ | 2022-08-01 | American journal of respiratory and critical care medicine |
| Diversity of approaches in artificial intelligence: an opportunity for discoveries in thoracic imaging. | Chassagnon G, Campredon A, Vakalopoulou M, Burgel PR | 2022-07-01 | The European respiratory journal |
| Inflammation biomarkers in sputum for clinical trials in cystic fibrosis: current understanding and gaps in knowledge. | Lepissier A, Addy C, Hayes K, Noel S, Bui S, Burgel PR, Dupont L, Eickmeier O, Fayon M, Leal T, Lopes C, Downey DG, Sermet-Gaudelus I | 2022-07-01 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Embolization of Recurrent Pulmonary Arteriovenous Malformations by Ethylene Vinyl Alcohol Copolymer (Onyx®) in Hereditary Hemorrhagic Telangiectasia: Safety and Efficacy. | Si-Mohamed SA, Cierco A, Gamondes D, Restier LM, Delagrange L, Cottin V, Dupuis-Girod S, Revel D | 2022-06-30 | Journal of personalized medicine |
| Trial of a Preferential Phosphodiesterase 4B Inhibitor for Idiopathic Pulmonary Fibrosis. | Richeldi L, Azuma A, Cottin V, Hesslinger C, Stowasser S, Valenzuela C, Wijsenbeek MS, Zoz DF, Voss F, Maher TM | 2022-06-09 | The New England journal of medicine |
| Respiratory management of spinal muscular atrophy type 1 patients treated with Nusinersen. | Menard J, Seferian AM, Fleurence E, Barzic A, Binoche A, Labouret G, Coutier L, Vuillerot C, Bieleu BM, Gomez Garcia de la Banda M, Corvol H, Servais L, Taytard J | 2022-06-01 | Pediatric pulmonology |
| CFTR Modulators in People with Cystic Fibrosis: Real-World Evidence in France. | Regard L, Martin C, Burnet E, Da Silva J, Burgel PR | 2022-05-28 | Cells |
| The role of cardiopulmonary exercise testing in identifying and monitoring pulmonary veno-oclusive disease: a case report with ING. | Segura de la Cal T, Pérez-Olivares C, Cristo Ropero MJ, Luna López R, Escribano-Subías P | 2022-05-01 | European heart journal. Case reports |
| Respiratory failure due to concomitant interstitial lung disease and diaphragmatic involvement in a patient with anti-MDA5 dermatomyositis: a case report. | Grignaschi S, Mongodi S, Alfonsi E, Mojoli F, Vertui V, Zanframundo G, Cavagna L | 2022-05-01 | Clinical and experimental rheumatology |
| Sustained effectiveness of elexacaftor-tezacaftor-ivacaftor in lung transplant candidates with cystic fibrosis. | Martin C, Reynaud-Gaubert M, Hamidfar R, Durieu I, Murris-Espin M, Danner-Boucher I, Chiron R, Leroy S, Douvry B, Grenet D, Mely L, Ramel S, Montcouquiol S, Lemonnier L, Burnet E, Paillasseur JL, Da Silva J, Burgel PR | 2022-05-01 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Systemic bis-phosphinic acid derivative restores chloride transport in Cystic Fibrosis mice. | da Cunha MF, Pranke I, Sassi A, Schreiweis C, Moriceau S, Vidovic D, Hatton A, Carlon MS, Creste G, Berhal F, Prestat G, Freund R, Odolczyk N, Jais JP, Gravier-Pelletier C, Zielenkiewicz P, Jullien V, Hinzpeter A, Oury F, Edelman A, Sermet-Gaudelus I | 2022-04-12 | Scientific reports |
| Safety and tolerability of nintedanib in patients with progressive fibrosing interstitial lung diseases: data from the randomized controlled INBUILD trial. | Cottin V, Martinez FJ, Jenkins RG, Belperio JA, Kitamura H, Molina-Molina M, Tschoepe I, Coeck C, Lievens D, Costabel U | 2022-04-07 | Respiratory research |
| Targeted therapy for pulmonary alveolar proteinosis: the time is now. | Bonella F, Borie R | 2022-04-01 | The European respiratory journal |
| Anetumab ravtansine versus vinorelbine in patients with relapsed, mesothelin-positive malignant pleural mesothelioma (ARCS-M): a randomised, open-label phase 2 trial. | Kindler HL, Novello S, Bearz A, Ceresoli GL, Aerts JGJV, Spicer J, Taylor P, Nackaerts K, Greystoke A, Jennens R, Calabrò L, Burgers JA, Santoro A, Cedrés S, Serwatowski P, Ponce S, Van Meerbeeck JP, Nowak AK, Blumenschein G, Siegel JM, Kasten L, Köchert K, Walter AO, Childs BH, Elbi C, Hassan R, Fennell DA | 2022-04-01 | The Lancet. Oncology |
| Tobramycin safety and efficacy review article. | Schwarz C, Taccetti G, Burgel PR, Mulrennan S | 2022-04-01 | Respiratory medicine |
| Determinants of survival after lung transplantation in telomerase-related gene mutation carriers: A retrospective cohort. | Phillips-Houlbracq M, Mal H, Cottin V, Gauvain C, Beier F, Sicre de Fontbrune F, Sidali S, Mornex JF, Hirschi S, Roux A, Weisenburger G, Roussel A, Wémeau-Stervinou L, Le Pavec J, Pison C, Marchand Adam S, Froidure A, Lazor R, Naccache JM, Jouneau S, Nunes H, Reynaud-Gaubert M, Le Borgne A, Boutboul D, Ba I, Boileau C, Crestani B, Kannengiesser C, Borie R | 2022-04-01 | American journal of transplantation : official journal of the American Society of Transplantation and the American Society of Transplant Surgeons |
| European Respiratory Society International Congress 2021: highlights from best-abstract awardees. | Ramakrishnan S, Beaufils F, De Brandt J, Viney K, Bradley C, Cottin V, Hassan M, Cruz J | 2022-03-01 | Breathe (Sheffield, England) |
| Pulmonary thromboendarterectomy in chronic thromboembolic pulmonary hypertension: the Spanish experience. | López-Gude MJ, Blanco I, Benito-Arnáiz V, Castellà M, Escribano-Subías P, Martin C, Barberà JA, Cortina-Romero JM | 2022-03-01 | Annals of cardiothoracic surgery |
| [French practical guidelines for the diagnosis and management of IPF - 2021 update, short version]. | Cottin V, Bonniaud P, Cadranel J, Crestani B, Jouneau S, Marchand-Adam S, Nunes H, Wémeau-Stervinou L, Bergot E, Blanchard E, Borie R, Bourdin A, Chenivesse C, Clément A, Gomez E, Gondouin A, Hirschi S, Lebargy F, Marquette CH, Montani D, Prévot G, Quetant S, Reynaud-Gaubert M, Salaun M, Sanchez O, Trumbic B, Berkani K, Brillet PY, Campana M, Chalabreysse L, Chatté G, Debieuvre D, Ferretti G, Fourrier JM, Just N, Kambouchner M, Legrand B, Le Guillou F, Lhuillier JP, Mehdaoui A, Naccache JM, Paganon C, Rémy-Jardin M, Si-Mohamed S, Terrioux P | 2022-03-01 | Revue des maladies respiratoires |
| Interstitial lung diseases associated with mutations of poly(A)-specific ribonuclease: A multicentre retrospective study. | Philippot Q, Kannengiesser C, Debray MP, Gauvain C, Ba I, Vieri M, Gondouin A, Naccache JM, Reynaud-Gaubert M, Uzunhan Y, Bondue B, Israël-Biet D, Dieudé P, Fourrage C, Lainey E, Manali E, Papiris S, Wemeau L, Hirschi S, Mal H, Nunes H, Schlemmer F, Blanchard E, Beier F, Cottin V, Crestani B, Borie R | 2022-03-01 | Respirology (Carlton, Vic.) |
| Major Decrease in Lung Transplantation for Patients with Cystic Fibrosis in France. | Martin C, Legeai C, Regard L, Cantrelle C, Dorent R, Carlier N, Kerbaul F, Burgel PR | 2022-03-01 | American journal of respiratory and critical care medicine |
| Natural history of respiratory muscle strength in spinal muscular atrophy: a prospective national cohort study. | Veldhoen ES, Wijngaarde CA, Hulzebos EHJ, Wösten-van Asperen RM, Wadman RI, van Eijk RPA, Asselman FL, Stam M, Otto LAM, Cuppen I, Scheijmans FEV, den Oudenrijn LPV, Bartels B, Gaytant MA, van der Ent CK, van der Pol WL | 2022-02-21 | Orphanet journal of rare diseases |
| Pirfenidone in Unclassifiable Interstitial Lung Disease: A Subgroup Analysis by Concomitant Mycophenolate Mofetil and/or Previous Corticosteroid Use. | Kreuter M, Maher TM, Corte TJ, Molina-Molina M, Axmann J, Gilberg F, Kirchgaessler KU, Cottin V | 2022-02-01 | Advances in therapy |
| Sjögren disease, not Sjögren's: comment on the article by Baer and Hammitt. | Cottin V | 2022-02-01 | Arthritis & rheumatology (Hoboken, N.J.) |
| Efficacy of Pirfenidone vs. Placebo in Unclassifiable Interstitial Lung Disease, by Surgical Lung Biopsy Status: Data From a post-hoc Analysis. | Molina-Molina M, Kreuter M, Cottin V, Corte TJ, Gilberg F, Kirchgaessler KU, Axmann J, Maher TM | 2022-01-01 | Frontiers in medicine |
| Are anaplastic lymphoma kinase (ALK) and O6-methylguanine-DNA methyltransferase (MGMT) promoter methylation driver biomarkers of pulmonary neuroendocrine tumors (NETs) and carcinomas (NECs)? | Hiddinga B, Zwaenepoel K, Janssens A, Van Meerbeeck J, Pauwels P | 2022-01-01 | Oncotarget |
| The Burden of Progressive-Fibrosing Interstitial Lung Diseases. | Cottin V, Teague R, Nicholson L, Langham S, Baldwin M | 2022-01-01 | Frontiers in medicine |
| Post hoc Analysis of Clinical Outcomes in Placebo- and Pirfenidone-Treated Patients with IPF Stratified by BMI and Weight Loss. | Jouneau S, Crestani B, Thibault R, Lederlin M, Vernhet L, Yang M, Morgenthien E, Kirchgaessler KU, Cottin V | 2022-01-01 | Respiration; international review of thoracic diseases |
| A call for evidence in connective tissue diseases-associated interstitial lung disease. | Cottin V, Lega JC, Coury F, Nasser M | 2022-01-01 | Joint bone spine |
| Real-world assessment of LCI following lumacaftor-ivacaftor initiation in adolescents and adults with cystic fibrosis. | Reix P, Tatopoulos A, Ioan I, Le Bourgeois M, Bui S, Choukroun ML, Bessaci-Kabouya K, Gerardin M, Bokov P, Da Silva J, Paillasseur JL, Burgel PR | 2022-01-01 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Impact of a high emergency lung transplantation programme for cystic fibrosis in France: insight from a comparison with Canada. | Coriati A, Sykes J, Lemonnier L, Ma X, Stanojevic S, Dehillotte C, Carlier N, Stephenson AL, Burgel PR | 2022-01-01 | The European respiratory journal |
| Interstitial pneumonia with autoimmune features: challenges and controversies. | Mackintosh JA, Wells AU, Cottin V, Nicholson AG, Renzoni EA | 2021-12-31 | European respiratory review : an official journal of the European Respiratory Society |
| Clinical utility of diagnostic biomarkers in malignant pleural mesothelioma: a systematic review and meta-analysis. | Schillebeeckx E, van Meerbeeck JP, Lamote K | 2021-12-31 | European respiratory review : an official journal of the European Respiratory Society |
| Spectral Photon-Counting CT Technology in Chest Imaging. | Si-Mohamed SA, Miailhes J, Rodesch PA, Boccalini S, Lacombe H, Leitman V, Cottin V, Boussel L, Douek P | 2021-12-09 | Journal of clinical medicine |
| Using chest CT scan and unsupervised machine learning for predicting and evaluating response to lumacaftor-ivacaftor in people with cystic fibrosis. | Campredon A, Battistella E, Martin C, Durieu I, Mely L, Marguet C, Belleguic C, Murris-Espin M, Chiron R, Fanton A, Bui S, Reynaud-Gaubert M, Reix P, Hoang-Thi TN, Vakalopoulou M, Revel MP, Da Silva J, Burgel PR, Chassagnon G | 2021-11-18 | The European respiratory journal |
| Long-term amikacin liposome inhalation suspension in cystic fibrosis patients with chronic P. aeruginosa infection. | Bilton D, Fajac I, Pressler T, Clancy JP, Sands D, Minic P, Cipolli M, Galeva I, Solé A, Quittner AL, Jumadilova Z, Ciesielska M, Konstan MW | 2021-11-01 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Patient perspectives following initiation of elexacaftor-tezacaftor-ivacaftor in people with cystic fibrosis and advanced lung disease. | Martin C, Burnet E, Ronayette-Preira A, de Carli P, Martin J, Delmas L, Prieur B, Burgel PR | 2021-11-01 | Respiratory medicine and research |
| Involvement of CFTR in the pathogenesis of pulmonary arterial hypertension. | Le Ribeuz H, To L, Ghigna MR, Martin C, Nagaraj C, Dreano E, Rucker-Martin C, Girerd B, Bouligand J, Pechoux C, Lambert M, Boet A, Issard J, Mercier O, Hoetzenecker K, Manoury B, Becq F, Burgel PR, Cottart CH, Olschewski A, Sermet-Gaudelus I, Perros F, Humbert M, Montani D, Antigny F | 2021-11-01 | The European respiratory journal |
| [se-atlas.de-Medical care atlas for people with rare diseases]. | Neff M, Schaaf J, Tegtbauer N, Schäfer J, Till M, Wagner TOF, Graeßner H, Mundlos C, Storf H | 2021-10-01 | Der Internist |
| Tuberous sclerosis complex for the pulmonologist. | Rebaine Y, Nasser M, Girerd B, Leroux C, Cottin V | 2021-09-30 | European respiratory review : an official journal of the European Respiratory Society |
| Recent developments in the treatment of small cell lung cancer. | Hiddinga BI, Raskin J, Janssens A, Pauwels P, Van Meerbeeck JP | 2021-09-30 | European respiratory review : an official journal of the European Respiratory Society |
| Improved survival albeit with persistent disparities in prognosis for people with cystic fibrosis in European countries. | Martin C, Burgel PR | 2021-09-01 | The European respiratory journal |
| Looking forward: key initiatives to improve the care of rare diseases and streamline the delivery of medicines and vaccines in Europe. | Humbert M, Simonds AK | 2021-09-01 | American journal of physiology. Lung cellular and molecular physiology |
| Updated guidance on the management of children with cystic fibrosis transmembrane conductance regulator-related metabolic syndrome/cystic fibrosis screen positive, inconclusive diagnosis (CRMS/CFSPID). | Barben J, Castellani C, Munck A, Davies JC, de Winter-de Groot KM, Gartner S, Kashirskaya N, Linnane B, Mayell SJ, McColley S, Ooi CY, Proesmans M, Ren CL, Salinas D, Sands D, Sermet-Gaudelus I, Sommerburg O, Southern KW | 2021-09-01 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Misconceptions regarding symptoms of sarcoidosis. | Drent M, Costabel U, Crouser ED, Grunewald J, Bonella F | 2021-08-01 | The Lancet. Respiratory medicine |
| Reply to Kuek et al.: Optimism with Caution: Elexacaftor-Tezacaftor-Ivacaftor in Patients with Advanced Pulmonary Disease. | Burgel PR, Da Silva J, Paillasseur JL, Martin C | 2021-08-01 | American journal of respiratory and critical care medicine |
| Radiological differences between chronic thromboembolic pulmonary disease (CTEPD) and chronic thromboembolic pulmonary hypertension (CTEPH). | Capone C, Valentini A, Spinillo SL, Klersy C, Celentano A, Pin M, Monterosso C, Dore R, Bassi EM, Zacchino M, Rodolico G, Corsico AG, Preda L, Ghio S, D'Armini AM | 2021-08-01 | European radiology |
| Low income and outcome in idiopathic pulmonary fibrosis: An association to uncover. | Sesé L, Caliez J, Annesi-Maesano I, Cottin V, Pesce G, Didier M, Carton Z, Israel-Biet D, Crestani B, Dudoret SG, Cadranel J, Wallaert B, Tazi A, Maître B, Prévot G, Marchand-Adam S, Hirschi S, Dury S, Giraud V, Gondouin A, Bonniaud P, Traclet J, Juvin K, Borie R, Bernaudin JF, Valeyre D, Cavalin C, Nunes H | 2021-07-01 | Respiratory medicine |
| Care Delivery Models and Interstitial Lung Disease: The Role of the Specialized Center. | Fisher JH, Cottin V | 2021-06-01 | Clinics in chest medicine |
| The role of cardiopulmonary exercise test in identifying pulmonary veno-occlusive disease. | Pérez-Olivares C, Segura de la Cal T, Flox-Camacho Á, Nuche J, Tenorio J, Martínez Meñaca A, Cruz-Utrilla A, de la Cruz-Bertolo J, Pérez Núñez M, Consortium SP, Arribas-Ynsaurriaga F, Escribano Subías P | 2021-06-01 | The European respiratory journal |
| Mental Well-being and General Health in Adolescents with Asthma: The Prevention and Incidence of Asthma and Mite Allergy Birth Cohort Study. | van der Laan SEI, de Hoog MLA, Nijhof SL, Gehring U, Vonk JM, van der Ent CK, Wijga AH | 2021-06-01 | The Journal of pediatrics |
| Estimates of epidemiology, mortality and disease burden associated with progressive fibrosing interstitial lung disease in France (the PROGRESS study). | Nasser M, Larrieu S, Boussel L, Si-Mohamed S, Bazin F, Marque S, Massol J, Thivolet-Bejui F, Chalabreysse L, Maucort-Boulch D, Hachulla E, Jouneau S, Le Lay K, Cottin V | 2021-05-24 | Respiratory research |
| PH CARE COVID survey: an international patient survey on the care for pulmonary hypertension patients during the early phase of the COVID-19 pandemic. | Godinas L, Iyer K, Meszaros G, Quarck R, Escribano-Subias P, Vonk Noordegraaf A, Jansa P, D'Alto M, Luknar M, Milutinov Ilic S, Belge C, Sitbon O, Reis A, Rosenkranz S, Pepke-Zaba J, Humbert M, Delcroix M | 2021-05-01 | Orphanet journal of rare diseases |
| Expectations about treatment of idiopathic pulmonary fibrosis: Comparative survey of patients, carers and physicians (the RESPIR French survey). | Cottin V, Bergot E, Bourdin A, Nunes H, Prévot G, Wallaert B, Marchand-Adam S | 2021-05-01 | Respiratory medicine and research |
| Educational aspects of rare and orphan lung diseases. | Alfaro TM, Wijsenbeek MS, Powell P, Stolz D, Hurst JR, Kreuter M, Moor CC | 2021-03-24 | Respiratory research |
| Safety of G-CSF with concurrent chemo-radiotherapy in limited-stage small cell lung cancer - Secondary analysis of the randomised phase 3 CONVERT trial. | Gomes F, Faivre-Finn C, Mistry H, Bezjak A, Pourel N, Fournel P, Van Meerbeeck J, Blackhall F | 2021-03-01 | Lung cancer (Amsterdam, Netherlands) |
| Clinical response to lumacaftor-ivacaftor in patients with cystic fibrosis according to baseline lung function. | Burgel PR, Durieu I, Chiron R, Mely L, Prevotat A, Murris-Espin M, Porzio M, Abely M, Reix P, Marguet C, Macey J, Sermet-Gaudelus I, Corvol H, Bui S, Biouhee T, Hubert D, Munck A, Lemonnier L, Dehillotte C, Silva JD, Paillasseur JL, Martin C | 2021-03-01 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Cystic Fibrosis Newborn Screening in Austria Using PAP and the Numeric Product of PAP and IRT Concentrations as Second-Tier Parameters. | Zeyda M, Schanzer A, Basek P, Bauer V, Eber E, Ellemunter H, Kallinger M, Riedler J, Thir C, Wadlegger F, Zacharasiewicz A, Renner S | 2021-02-13 | Diagnostics (Basel, Switzerland) |
| Hemodynamic Response to Treatment and Outcomes in Pulmonary Hypertension Associated With Interstitial Lung Disease Versus Pulmonary Arterial Hypertension in Systemic Sclerosis: Data From a Study Identifying Prognostic Factors in Pulmonary Hypertension Associated With Interstitial Lung Disease. | Chauvelot L, Gamondes D, Berthiller J, Nieves A, Renard S, Catella-Chatron J, Ahmad K, Bertoletti L, Camara B, Gomez E, Launay D, Montani D, Mornex JF, Prévot G, Sanchez O, Schott AM, Subtil F, Traclet J, Turquier S, Zeghmar S, Habib G, Reynaud-Gaubert M, Humbert M, Cottin V | 2021-02-01 | Arthritis & rheumatology (Hoboken, N.J.) |
| Radiological Findings in Multidetector Computed Tomography (MDCT) of Hereditary and Sporadic Pulmonary Veno-Occlusive Disease: Certainties and Uncertainties. | Pérez Núñez M, Alonso Charterina S, Pérez-Olivares C, Revilla Ostolaza Y, Morales Ruiz R, Enguita Valls AB, Tenorio JA, Gallego Zazo N, De Pablo Gafas A, Lapunzina P, Rodríguez Chaverri A, Escribano Subías P | 2021-01-19 | Diagnostics (Basel, Switzerland) |
| Mortality and Respiratory-Related Hospitalizations in Idiopathic Pulmonary Fibrosis Not Treated With Antifibrotics. | Cottin V, Spagnolo P, Bonniaud P, Nolin M, Dalon F, Kirchgässler KU, Kamath TV, Van Ganse E, Belhassen M | 2021-01-01 | Frontiers in medicine |
| Variability in Global Prevalence of Interstitial Lung Disease. | Kaul B, Cottin V, Collard HR, Valenzuela C | 2021-01-01 | Frontiers in medicine |
| Epidemiology, Mortality and Healthcare Resource Utilization Associated With Systemic Sclerosis-Associated Interstitial Lung Disease in France. | Cottin V, Larrieu S, Boussel L, Si-Mohamed S, Bazin F, Marque S, Massol J, Thivolet-Bejui F, Chalabreysse L, Maucort-Boulch D, Jouneau S, Hachulla E, Chollet J, Nasser M | 2021-01-01 | Frontiers in medicine |
| Gender Differences in Idiopathic Pulmonary Fibrosis: Are Men and Women Equal? | Sesé L, Nunes H, Cottin V, Israel-Biet D, Crestani B, Guillot-Dudoret S, Cadranel J, Wallaert B, Tazi A, Maître B, Prévot G, Marchand-Adam S, Hirschi S, Dury S, Giraud V, Gondouin A, Bonniaud P, Traclet J, Juvin K, Borie R, Carton Z, Freynet O, Gille T, Planès C, Valeyre D, Uzunhan Y | 2021-01-01 | Frontiers in medicine |
| The Experience, Prerequisites, and the Barriers in Organizing a Specialized Rehabilitation Program for Patients with Pulmonary Hypertension. | Palevičiūtė E, Gumbienė L, Jurevičienė E, Šimbelytė T, Laucevičienė I, Laucevičius A, Barysienė J, Eichstaedt CA, Benjamin N, Grünig E, Čelutkienė J | 2021-01-01 | Respiration; international review of thoracic diseases |
| Concurrence of 1- and 3-Min Sit-to-Stand Tests with the 6-Min Walk Test in Idiopathic Pulmonary Fibrosis. | Fedi A, Keddache S, Quétant S, Guillien A, Antoniadis A, Soumagne T, Ritter O, Glérant JC, Cottin V, Degano B, Aguilaniu B | 2021-01-01 | Respiration; international review of thoracic diseases |
| Update on Respiratory Fungal Infections in Cystic Fibrosis Lung Disease and after Lung Transplantation. | Renner S, Nachbaur E, Jaksch P, Dehlink E | 2020-12-21 | Journal of fungi (Basel, Switzerland) |
| Quantification of Cystic Fibrosis Lung Disease with Radiomics-based CT Scores. | Chassagnon G, Zacharaki EI, Bommart S, Burgel PR, Chiron R, Dangeard S, Paragios N, Martin C, Revel MP | 2020-12-01 | Radiology. Cardiothoracic imaging |
| Reduced Intestinal Inflammation With Lumacaftor/Ivacaftor in Adolescents With Cystic Fibrosis. | Tétard C, Mittaine M, Bui S, Beaufils F, Maumus P, Fayon M, Burgel PR, Lamireau T, Delhaes L, Mas E, Enaud R | 2020-12-01 | Journal of pediatric gastroenterology and nutrition |
| Feasibility of a Noninvasive Operability Assessment in Chronic Thromboembolic Pulmonary Hypertension under Real-World Practice. | Rodriguez Chaverri A, Revilla Ostolaza Y, Lopez-Gude MJ, Velazquez MT, Ponz de Antonio I, Alonso Charterina S, Albarran Gonzalez-Trevilla A, Perez Nunez M, Perez Vela JL, Morales Ruiz R, Delgado Jimenez JF, Arribas Ynsaurriaga F, Cortina JM, Escribano Subias P | 2020-10-21 | Diagnostics (Basel, Switzerland) |
| Urinary Exosomes of Patients with Cystic Fibrosis Unravel CFTR-Related Renal Disease. | Gauthier S, Pranke I, Jung V, Martignetti L, Stoven V, Nguyen-Khoa T, Semeraro M, Hinzpeter A, Edelman A, Guerrera IC, Sermet-Gaudelus I | 2020-09-10 | International journal of molecular sciences |
| Current treatment of sarcoidosis. | Sellarés J, Francesqui J, Llabres M, Hernandez-Gonzalez F, Baughman RP | 2020-09-01 | Current opinion in pulmonary medicine |
| R117H-CFTR function and response to VX-770 correlate with mRNA and protein expression in intestinal organoids. | Van Mourik P, van Haaren P, Kruisselbrink E, Korkmaz C, Janssens HM, de Winter-de Groot KM, van der Ent CK, Hagemeijer MC, Beekman JM | 2020-09-01 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Prediction of Prognostic Hemodynamic Indices in Pulmonary Hypertension Using Non-Invasive Parameters. | Mańczak R, Kurzyna M, Piłka M, Darocha S, Florczyk M, Wieteska-Miłek M, Mańczak M, Torbicki A | 2020-08-27 | Diagnostics (Basel, Switzerland) |
| Desquamative interstitial pneumonia: a systematic review of its features and outcomes. | Hellemons ME, Moor CC, von der Thüsen J, Rossius M, Odink A, Thorgersen LH, Verschakelen J, Wuyts W, Wijsenbeek MS, Bendstrup E | 2020-06-30 | European respiratory review : an official journal of the European Respiratory Society |
| Diagnostic approach of fibrosing interstitial lung diseases of unknown origin. | Cottin V, Valenzuela C | 2020-06-01 | Presse medicale (Paris, France : 1983) |
| Patients' and Healthcare Professionals' Experiences of Idiopathic Pulmonary Fibrosis Treatment with the Pirfenidone 801 mg Tablet Formulation: A Multinational Survey. | Lancaster LH, Valenzuela C, Mason W, Neurohr C, Ripamonti E, Kirchgaessler KU, Cottin V | 2020-06-01 | Pulmonary therapy |
| Impact of COVID-19 on people with cystic fibrosis. | Colombo C, Burgel PR, Gartner S, van Koningsbruggen-Rietschel S, Naehrlich L, Sermet-Gaudelus I, Southern KW | 2020-05-01 | The Lancet. Respiratory medicine |
| Antimicrobial resistance in cystic fibrosis: A Delphi approach to defining best practices. | Zemanick E, Burgel PR, Taccetti G, Holmes A, Ratjen F, Byrnes CA, Waters VJ, Bell SC, VanDevanter DR, Stuart Elborn J, Flume PA | 2020-05-01 | Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society |
| Getting neural about airway gland secretion. | Amatngalim GD, Ribeiro CMP | 2020-04-01 | The European respiratory journal |
| Prolidase deficiency: a new genetic cause of combined pulmonary fibrosis and emphysema syndrome in the adult. | Cottin V, Nasser M, Traclet J, Chalabreysse L, Lèbre AS, Si-Mohamed S, Philit F, Thivolet-Béjui F | 2020-04-01 | The European respiratory journal |
| CheckMate 171: A phase 2 trial of nivolumab in patients with previously treated advanced squamous non-small cell lung cancer, including ECOG PS 2 and elderly populations. | Felip E, Ardizzoni A, Ciuleanu T, Cobo M, Laktionov K, Szilasi M, Califano R, Carcereny E, Griffiths R, Paz-Ares L, Duchnowska R, Garcia MA, Isla D, Jassem J, Appel W, Milanowski J, Van Meerbeeck JP, Wolf J, Li A, Acevedo A, Popat S | 2020-03-01 | European journal of cancer (Oxford, England : 1990) |
| Genetic diagnosis in practice: From cystic fibrosis to CFTR-related disorders. | Pagin A, Sermet-Gaudelus I, Burgel PR | 2020-02-01 | Archives de pediatrie : organe officiel de la Societe francaise de pediatrie |
| Real-Life Safety and Effectiveness of Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis. | Burgel PR, Munck A, Durieu I, Chiron R, Mely L, Prevotat A, Murris-Espin M, Porzio M, Abely M, Reix P, Marguet C, Macey J, Sermet-Gaudelus I, Corvol H, Bui S, Lemonnier L, Dehillotte C, Da Silva J, Paillasseur JL, Hubert D | 2020-01-15 | American journal of respiratory and critical care medicine |
| Risk and outcome of COVID-19 infection in sarcoidosis patients: results of a self-reporting questionnaire. | Baughman RP, Lower EE, Buchanan M, Rottoli P, Drent M, Sellares J, Terwiel M, Elfferich M, Francesqui J, Barriuso Cabrerizo MR, Sweiss N, Martone F, Al-Hakim T, Judson MA | 2020-01-01 | Sarcoidosis, vasculitis, and diffuse lung diseases : official journal of WASOG |
| Validation of short- and long-term demographic forecasts using the Canadian Cystic Fibrosis Registry. | Martelli V, Sykes J, Burgel PR, Bellis G, Coriati A, Stanojevic S, Stephenson AL | 2020-01-01 | The European respiratory journal |
| Cystic Fibrosis Diagnosis in Newborns, Children, and Adults. | Castellani C, Linnane B, Pranke I, Cresta F, Sermet-Gaudelus I, Peckham D | 2019-12-01 | Seminars in respiratory and critical care medicine |
| Tumour Treating Fields in combination with pemetrexed and cisplatin or carboplatin as first-line treatment for unresectable malignant pleural mesothelioma (STELLAR): a multicentre, single-arm phase 2 trial. | Ceresoli GL, Aerts JG, Dziadziuszko R, Ramlau R, Cedres S, van Meerbeeck JP, Mencoboni M, Planchard D, Chella A, Crinò L, Krzakowski M, Rüssel J, Maconi A, Gianoncelli L, Grosso F | 2019-12-01 | The Lancet. Oncology |
| Association between surgical volume and post-operative mortality and survival after surgical resection in lung cancer in Belgium: A population-based study. | Schillemans V, Vrijens F, De Gendt C, Robays J, Silversmit G, Verleye L, Camberlin C, Dubois C, Stordeur S, Wauters I, Van Meerbeeck JP, Van Eycken E, De Leyn P | 2019-12-01 | European journal of surgical oncology : the journal of the European Society of Surgical Oncology and the British Association of Surgical Oncology |
| Influence of Antisynthetase Antibodies Specificities on Antisynthetase Syndrome Clinical Spectrum Time Course. | Cavagna L, Trallero-Araguás E, Meloni F, Cavazzana I, Rojas-Serrano J, Feist E, Zanframundo G, Morandi V, Meyer A, Pereira da Silva JA, Matos Costa CJ, Molberg O, Andersson H, Codullo V, Mosca M, Barsotti S, Neri R, Scirè C, Govoni M, Furini F, Lopez-Longo FJ, Martinez-Barrio J, Schneider U, Lorenz HM, Doria A, Ghirardello A, Ortego-Centeno N, Confalonieri M, Tomietto P, Pipitone N, Rodriguez Cambron AB, Blázquez Cañamero MÁ, Voll RE, Wendel S, Scarpato S, Maurier F, Limonta M, Colombelli P, Giannini M, Geny B, Arrigoni E, Bravi E, Migliorini P, Mathieu A, Piga M, Drott U, Delbrueck C, Bauhammer J, Cagnotto G, Vancheri C, Sambataro G, De Langhe E, Sainaghi PP, Monti C, Gigli Berzolari F, Romano M, Bonella F, Specker C, Schwarting A, Villa Blanco I, Selmi C, Ceribelli A, Nuno L, Mera-Varela A, Perez Gomez N, Fusaro E, Parisi S, Sinigaglia L, Del Papa N, Benucci M, Cimmino MA, Riccieri V, Conti F, Sebastiani GD, Iuliano A, Emmi G, Cammelli D, Sebastiani M, Manfredi A, Bachiller-Corral J, Sifuentes Giraldo WA, Paolazzi G, Saketkoo LA, Giorgi R, Salaffi F, Cifrian J, Caporali R, Locatelli F, Marchioni E, Pesci A, Dei G, Pozzi MR, Claudia L, Distler J, Knitza J, Schett G, Iannone F, Fornaro M, Franceschini F, Quartuccio L, Gerli R, Bartoloni E, Bellando Randone S, Zampogna G, Gonzalez Perez MI, Mejia M, Vicente E, Triantafyllias K, Lopez-Mejias R, Matucci-Cerinic M, Selva-O'Callaghan A, Castañeda S, Montecucco C, Gonzalez-Gay MA | 2019-11-18 | Journal of clinical medicine |
| Precision medicine: The future of diagnostic approach to pulmonary hypertension? | Kedzierski P, Torbicki A | 2019-09-01 | Anatolian journal of cardiology |
| Where are the gaps in education in the field of rare lung disease? Perspectives from the ERN-LUNG educational programme survey. | Powell P, Kreuter M, Wijsenbeek-Lourens M | 2019-06-01 | Breathe (Sheffield, England) |
| The Ariane-IPF ERS Clinical Research Collaboration: seeking collaboration through launch of a federation of European registries on idiopathic pulmonary fibrosis. | Cottin V, Annesi-Maesano I, Günther A, Galvin L, Kreuter M, Powell P, Prasse A, Reynolds G, Richeldi L, Spagnolo P, Valenzuela C, Wijsenbeek M, Wuyts WA, Crestani B | 2019-05-01 | The European respiratory journal |
