Expert management of congenital portosystemic shunts and their complications.

(JHEP reports : innovation in hepatology, v6.1:100933)

Congenital portosystemic shunts are often associated with systemic complications, the most challenging of which are liver nodules, pulmonary hypertension, endocrine abnormalities, and neurocognitive dysfunction. In the present paper, we offer expert clinical guidance on the management of liver nodules, pulmonary hypertension, and endocrine abnormalities, and we make recommendations regarding shunt closure and follow-up.

© 2023 The Author(s).

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TitleExpert management of congenital portosystemic shunts and their complications.
Date2024-01-01
Issue nameJHEP reports : innovation in hepatology
Issue numberv6.1:100933
DOI10.1016/j.jhepr.2023.100933
PubMed38234409
AuthorsMcLin VA, Franchi-Abella S, Brütsch T, Bahadori A, Casotti V, de Ville de Goyet J, Dumery G, Gonzales E, Guérin F, Hascoet S, Heaton N, Kuhlmann B, Lador F, Lambert V, Marra P, Plessier A, Quaglia A, Rougemont AL, Savale L, Sarma MS, Sitbon O, Superina RA, Uchida H, van Albada M, van der Doef HPJ, Vilgrain V, Wacker J, Zwaveling N, Debray D & Wildhaber BE
Keywordsadenoma, congenital portosystemic shunt, focal nodular hyperplasia, hepatocellular carcinoma, hyperandrogenism, hyperinsulinism, hypoglycemia, occlusion test, portal pressure, puberty, pulmonary hypertension, β-catenin
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